我們報告了一例腎臟的原始神經外胚層腫瘤，病患因右腰痛來院求診。術前檢查包括超音波、電腦斷層、血管攝影，皆顯示一右側腎臟腫瘤。術後一年並無復發及轉移。我們報告這個病例並回顧文獻。

We report on a cese of a 36-year-old female patient with the chief complaint of right loin pain for 1 week. The image studies with ultrasound, computed tomography, and angiography all revealed a right renal mass. The pathological finding was a primitive neuroectodermal tumor (PNET) of the right kidney. The patient was well without recurrence or metastatic disease 1year after surgery. We report on this case and review the literature.