馬蹄腎在臨床上常併發水腎、腎結石及尿路感染，本文提出一病例報告。病人出現無痛血尿，經腎臟腎盂攝影及腹部電腦斷層診斷為馬蹄腎併左腎盂腫瘤。經腎動脈攝影確定腎血管之解剖結構，採經腹膜手術阻斷左腎血流供給，暫時阻斷腎峽部動脈而成功摘除左腎。術後追蹤九個月，至今無復發。

Horseshoe kidney, afrequent abnormality of renalfusion, is often complicated with hydronephrosis, renal stone and urinary infection. This report concerns a horseshoe kidney with transitional cell carcinoma. The patient presented as a painless, gross hematuria, diagnosed to be horseshoe kidney with left renal pelvis and lower calyx tumor. The vascular anatomy was confirmed by renal angiography. Left nephroureterectomy and bladder cuff excision was sucessfully performed through a transperitoneal approach for vascular control and precise demarcation of the line of resection at the isthmus. Follow- up by computerized tomography nine months post-operatively revealed no tumor recurrence.