膽道內出血是一種少見的疾病。造成此病的原因大致上可分為三類:創傷性、自發性和發炎性。我們在此提出一個案，一位35歲有A型血友病的男性併發自發性的膽囊內出血。他是由於類似膽囊炎的症狀而來急診室求醫。經由腹部超音波和電腦斷層的檢查，診斷出膽囊內出血。經過適當的保守治療之後，病人順利的康復。當急診醫師面臨有出血性疾病的患者表現出右上腹痛、上消化道出血和黃痘時，應該把自發性膽道內和膽囊內出血列入鑑別診斷之中。

The hemobilia is a rare condition. It is generally caused by three categories: trauma, spontaneous or inflammation. Herein, we reported a case of the spontaneous intracholecystic hemorrhage in a 35-year-old male with hemophilia A. He presented the symptoms mimicking an acute cholecystitis. The abdominal sonography and computed tomography disclosed the intracholecystic hemorrhage. After conservative treatment, he recovered uneventfully. Emergency physicians should keep in mind about spontaneous hemorrhage into the biliary tract or gallbladder as a possibility for their differential diagnosis of patients with coagulopathy who presented with the triad of right upper quadrant pain, upper gastrointestinal bleeding and jaundice.