戒指細胞型臍尿管腺癌在臍尿管腺癌中是極少見的一類。目前在文獻報告上僅發表27例。我們報告一位62歲男性因臍尿管腺癌接受部分膀胱切除及臍尿管整體切除。病人在五個月後局部復發並接受緩和經尿道膀胱腫瘤切除及局部放射線治療。追蹤病人電腦斷層顯示復發的腫瘤有明顯的縮小。診斷22個月後病人目前仍存活且無症狀。我們回顧文獻上相關報告並整理分析此疾病之臨床表現、治療方式及預後。

Signet ring cell adenocarcinomas of the urachus are an extremely rare variety of urachal carcinoma with only 27 cases reported in the literature to date. We present 1 case of a 62-year-old man treated initially by transurethral resection (TUR) followed by a partial cystectomy with en bloc excision of the urachus and umbilicus. Local recurrence occurred 5 months later, and he received palliative TUR and regional radiotherapy. Shrinkage of the residual tumor was documented, and he is still alive and well 22 months after the initial diagnosis. Clinical features, treatment modalities, and the prognosis of this rare disease are reviewed.